Ependymoma
Ependymoma is a type of brain tumour formed from ependymal cells in the brain, which produce cerebrospinal fluid. It is the third most common type of childhood brain tumour. The average age of diagnosis is five years old.
On this page:
- What is an ependymoma?
- Ependymoma grading
- Ependymoma tumour symptoms
- Ependymoma treatment
- Ependymoma causes
- How long can someone live with an ependymoma?
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If your child or a child you know has recently been diagnosed with an ependymoma, you may be worried about what this means. This is a natural way to feel. Our Children and Families team can help answer any questions you may have or provide a listening ear if you need one.
What is an ependymoma?
Ependymomas are a type of brain tumour that are formed from the ependymal cells. These are the brain cells that produce cerebrospinal fluid (CSF).
You might sometimes hear an this type of tumour called a glioma.
These tumours are usually:
- slow growing
- less likely to spread.
While they can develop at any age, the average age of diagnosis is 5 years old and at least a quarter of diagnoses happen before the age of 2.
Most childhood ependymomas are found in the hindbrain (also called the posterior fossa). This area controls functions like balance, movement, breathing and blood pressure.
Ependymoma grading
There are four different types of ependymoma, which fit into three different grades.
You might hear your child’s doctor call the brain tumour by a more specific name. This could be:
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Subependymomas are grade 1 ependymomas that are relatively uncommon in children and appear most often near a ventricle.
Myxopapillary ependymoms are grade 1 ependymomas that are also relatively uncommon in children and usually develop in the lower part of the spinal column.
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These are the most common type of ependymoma tumour and usually appear close to, or in, a ventricle in the hindbrain.
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Also known as anaplastic ependymomas, these are the fastest growing ependymal tumour and also commonly grow in the hindbrain.
Ependymoma tumour symptoms
Most child ependymomas develop along the ventricle in the hindbrain known as the fourth ventricle. Depending on where the tumour is located, your child might have one or more of the following symptoms:
- Their head seeming to be twisted or tilted (known as torticollis or wry neck)
- Loss of balance (known as ataxia)
- Problems speaking (known as dysarthria)
- Difficulty swallowing (known as dysphagia)
- Making overly clumsy movements (known as dysmetria)
- Headaches
- Seizures
- Vision problems, like double vision
- Nausea or vomiting
They may also experience some of the general symptoms of childhood brain tumours.
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Ependymoma treatment
Ependymoma treatment often involves the following:
- Surgery
- Radiotherapy
- Chemotherapy
The first treatment your child is likely to have is surgery to remove as much of the tumour as possible. If the tumour is low grade and the surgeon is able to remove all the tumour, your child may not need any other treatment.
If it’s not possible to remove all the tumour or if the tumour is high grade, then surgery may be followed by radiotherapy or chemotherapy.
Ependymoma causes
There is nothing you or your child have done, or could’ve avoiding doing, that would have stopped an ependymoma from growing.
As with any brain tumour, we aren’t sure why they begin to develop, although research is helping us to understand some of the risk factors involved.
How long can somebody live with an ependymoma?
This is affected by many factors. It depends on the grade, size and location of the tumour. It also depends on your or your child’s body’s unique response to treatment and how healthy you are in general.
Find out more by clicking the button below.
More information
Ependymoma in children factsheet – PDF
Find out more about Ependymoma in children in the full factsheet.
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